Subacute Sclerosing Panencephalitis

Subakut skleroserande panencefalit

Engelsk definition

A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)

Svenska synonymer

SSPE

Engelska synonymer

Panencephalitides, Subacute Sclerosing Sclerosing Panencephalitides, Subacute Subacute Sclerosing Panencephalitides Van Bogaert's Leukoencephalitis Van Bogaert Leukoencephalitis Van Bogaerts Leukoencephalitis SSPE Sclerosing Panencephalitis, Subacute Encephalitis, Inclusion Body, Measles Sclerosing Leukoencephalitis, Subacute Leukoencephalitides, Subacute Sclerosing Sclerosing Leukoencephalitides, Subacute Subacute Sclerosing Leukoencephalitides Subacute Sclerosing Leukoencephalitis Leukoencephalitis, Subacute Sclerosing Measles Inclusion Body Encephalitis Inclusion Body Encephalitis, Measles Leukoencephalitis, Van Bogaert's Leukoencephalitis, Van Bogaert Leukoencephalitis, Van Bogaerts Panencephalitis, Subacute Sclerosing