Engelsk definition
A degenerative disease of the central nervous system characterized by balance difficulties; OCULAR MOTILITY DISORDERS (supranuclear ophthalmoplegia); DYSARTHRIA; swallowing difficulties; and axial DYSTONIA. Onset is usually in the fifth decade and disease progression occurs over several years. Pathologic findings include neurofibrillary degeneration and neuronal loss in the dorsal MESENCEPHALON; SUBTHALAMIC NUCLEUS; RED NUCLEUS; pallidum; dentate nucleus; and vestibular nuclei. (From Adams et al., Principles of Neurology, 6th ed, pp1076-7)
Svenska synonymer
Steele-Richardson-Olszewskis syndrom
Engelska synonymer
Progressive Supranuclear Palsies — Supranuclear Palsies, Progressive — Steele-Richardson-Olszewski Syndrome — Steele Richardson Olszewski Syndrome — Richardson's Syndrome — Richardson Syndrome — Steele-Richardson-Olszewski Disease — Steele Richardson Olszewski Disease — Palsy, Progressive Supranuclear — Progressive Supranuclear Palsy — Ophthalmoplegia, Progressive Supranuclear — Supranuclear Ophthalmoplegia, Progressive — Progressive Supranuclear Ophthalmoplegia — Supranuclear Palsy, Progressive, 1 — Progressive Supranuclear Palsy 1