Waldenstrom Macroglobulinemia

Waldenströms makroglobulinemi

Svensk definition

En lymfoproliferativ rubbning som karakteriseras av onormala plasmaceller och pleomorfa B-lymfocyter, höjda nivåer av immunoglobulin M. Också känd som lymfoplasmatiskt lymfom. Kliniska tecken inkluderar blodbrist, blödningar and hyperviskositet.

Engelsk definition

A lymphoproliferative disorder characterized by pleomorphic B-LYMPHOCYTES including PLASMA CELLS, with increased levels of monoclonal serum IMMUNOGLOBULIN M. There is lymphoplasmacytic cells infiltration into bone marrow and often other tissues, also known as lymphoplasmacytic lymphoma. Clinical features include ANEMIA; HEMORRHAGES; and hyperviscosity.

Svenska synonymer

Makroglobulinemi Waldenströms sjukdom Lymfoplasmacytisk lymfom Familjär Waldenströms makroglobulinemi

Engelska synonymer

Macroglobulinemia, Waldenstrom Lymphoma, Lymphoplasmacytoid Lymphomas, Lymphoplasmacytoid Lymphoplasmacytoid Lymphoma Lymphoplasmacytoid Lymphomas Macroglobulinemia Waldenstrom's Macroglobulinemia Macroglobulinemia, Waldenstrom's Waldenstroms Macroglobulinemia Waldenstrom's Macroglobulinaemia Macroglobulinaemia, Waldenstrom's Waldenstrom Macroglobulinaemia Waldenstroms Macroglobulinaemia Lymphoma, Lymphocytic, Plasmacytoid Primary Macroglobulinemia Macroglobulinemia, Primary Familial Waldenstrom's Macroglobulinaemia Familial Waldenstrom Macroglobulinaemia Familial Waldenstroms Macroglobulinaemia Macroglobulinaemia, Familial Waldenstrom's Waldenstrom's Macroglobulinaemia, Familial