Mitochondrial Trifunctional Protein

Engelsk definition

A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS.

Svenska synonymer

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Engelska synonymer

Trifunctional Protein, Mitochondrial Mitochondrial Long Chain Enoyl CoA Hydratase 3 Hydroxyacyl CoA Dehydrogenase 3 Ketoacyl CoA Thiolase Trifunctional Protein FA beta-OMC Mitochondrial Fatty Acid beta-Oxidation Trifunctional Protein Mitochondrial Fatty Acid beta Oxidation Trifunctional Protein