Complement C1 Inhibitor Protein

C1-INH-protein

Engelsk definition

An endogenous 105-kDa plasma glycoprotein produced primarily by the LIVER and MONOCYTES. It inhibits a broad spectrum of proteases, including the COMPLEMENT C1R and the COMPLEMENT C1S proteases of the CLASSICAL COMPLEMENT PATHWAY, and the MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES. C1-INH-deficient individuals suffer from HEREDITARY ANGIOEDEMA TYPES I AND II.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Serpin Family G Member 1 — C1 Esterase Inhibitor — Esterase Inhibitor, C1 — C1-Inhibitor Protein — C1 Inhibitor Protein — Serpin G1 — Plasma Protease C1 Inhibitor — Complement C1-Inhibitor Protein — SERPING1 — C1-INH Protein — C1 INH Protein