En grupp elakartade tumörer i nervsystemet som uppvisar primitiva celler med inslag av nervcells- och/eller gliacellsdifferentiering. Några författare begränsar bruket av denna term till tumörer i det centrala nervsystemet, medan andra låter den omfatta tumörer av liknande ursprung utanför skallen, t ex neuroepiteliom. Termen används även ibland som synonym för medulloblastom. I allmänhet uppstår dessa tumörer under de första tio åren av livet och brukar vara mycket maligna.
A group of malignant tumors of the nervous system that feature primitive cells with elements of neuronal and/or glial differentiation. Use of this term is limited by some authors to central nervous system tumors and others include neoplasms of similar origin which arise extracranially (i.e., NEUROECTODERMAL TUMORS, PRIMITIVE, PERIPHERAL). This term is also occasionally used as a synonym for MEDULLOBLASTOMA. In general, these tumors arise in the first decade of life and tend to be highly malignant. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2059)
Ependymoblastom — Primitiva neuroepiteliala tumörer — Spongioblastom
Neuroectodermal Tumor, Primitive — Primitive Neuroectodermal Tumor — Primitive Neuroectodermal Tumors — Tumor, Primitive Neuroectodermal — Tumors, Primitive Neuroectodermal — Primitive Neuroepithelial Neoplasms — Neuroepithelial Tumors, Primitive — Neuroepithelial Tumor, Primitive — Primitive Neuroepithelial Tumor — Primitive Neuroepithelial Tumors — Tumor, Primitive Neuroepithelial — Tumors, Primitive Neuroepithelial — PNET — PNETs — Neoplasms, Primitive Neuroepithelial — Neoplasm, Primitive Neuroepithelial — Neuroepithelial Neoplasm, Primitive — Primitive Neuroepithelial Neoplasm — Neuroepithelial Neoplasms, Primitive — Medulloepithelioma — Medulloepitheliomas — Cerebral Primitive Neuroectodermal Tumor — Ependymoblastoma — Ependymoblastomas — Spongioblastoma — Spongioblastomas