Neuroectodermal Tumors, Primitive

Primitiva neuroektodermala tumörer

Svensk definition

En grupp elakartade tumörer i nervsystemet som uppvisar primitiva celler med inslag av nervcells- och/eller gliacellsdifferentiering. Några författare begränsar bruket av denna term till tumörer i det centrala nervsystemet, medan andra låter den omfatta tumörer av liknande ursprung utanför skallen, t ex neuroepiteliom. Termen används även ibland som synonym för medulloblastom. I allmänhet uppstår dessa tumörer under de första tio åren av livet och brukar vara mycket maligna.

Engelsk definition

A group of malignant tumors of the nervous system that feature primitive cells with elements of neuronal and/or glial differentiation. Use of this term is limited by some authors to central nervous system tumors and others include neoplasms of similar origin which arise extracranially (i.e., NEUROECTODERMAL TUMORS, PRIMITIVE, PERIPHERAL). This term is also occasionally used as a synonym for MEDULLOBLASTOMA. In general, these tumors arise in the first decade of life and tend to be highly malignant. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2059)

Svenska synonymer

Ependymoblastom Primitiva neuroepiteliala tumörer Spongioblastom

Engelska synonymer

Neuroectodermal Tumor, Primitive Primitive Neuroectodermal Tumor Primitive Neuroectodermal Tumors Tumor, Primitive Neuroectodermal Tumors, Primitive Neuroectodermal Primitive Neuroepithelial Neoplasms Neuroepithelial Tumors, Primitive Neuroepithelial Tumor, Primitive Primitive Neuroepithelial Tumor Primitive Neuroepithelial Tumors Tumor, Primitive Neuroepithelial Tumors, Primitive Neuroepithelial PNET PNETs Neoplasms, Primitive Neuroepithelial Neoplasm, Primitive Neuroepithelial Neuroepithelial Neoplasm, Primitive Primitive Neuroepithelial Neoplasm Neuroepithelial Neoplasms, Primitive Medulloepithelioma Medulloepitheliomas Cerebral Primitive Neuroectodermal Tumor Ependymoblastoma Ependymoblastomas Spongioblastoma Spongioblastomas