En typ av fibrosarkom i huden, som oftast börjar som en förhårdnad knöl som växer långsamt och därför ofta förbises tills den blivit stor. Dermatofibrosarkom visar en extremt aggressiv benägenhet att invadera omgivande vävnad. Tumörerna bildar dock ej metastaser, inte ens efter upprepade återkomster. Ca 50% återkommer efter enkelt kirurgiskt insnitt; därför bör en omfattande excision (utskärning) göras. omfattande.
A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.
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Dermatofibrosarcomas — Darier-Hoffmann Tumor — Darier Hoffmann Tumor — Tumor, Darier-Hoffmann — Dermatofibrosarcoma Protuberan — Dermatofibrosarcoma Protuberans — Protuberan, Dermatofibrosarcoma — Protuberans, Dermatofibrosarcoma — Darier-Ferrand Tumor — Darier Ferrand Tumor — Tumor, Darier-Ferrand — Metastatic Dermatofibrosarcoma Protuberans — Dermatofibrosarcoma Protuberan, Metastatic — Dermatofibrosarcoma Protuberans, Metastatic — Metastatic Dermatofibrosarcoma Protuberan — Protuberan, Metastatic Dermatofibrosarcoma — Protuberans, Metastatic Dermatofibrosarcoma — FS-DFSP — Fibrosarcomatous Dermatofibrosarcoma Protuberans — Dermatofibrosarcoma Protuberans, Fibrosarcomatous — Dermatofibrosarcoma Protuberan, Fibrosarcomatous — Fibrosarcomatous Dermatofibrosarcoma Protuberan — Protuberan, Fibrosarcomatous Dermatofibrosarcoma — Protuberans, Fibrosarcomatous Dermatofibrosarcoma — DFSP, Fibrosarcomatous — DFSPs, Fibrosarcomatous — Fibrosarcomatous DFSP — Fibrosarcomatous DFSPs — Giant Cell Fibroblastoma — Cell Fibroblastoma, Giant — Cell Fibroblastomas, Giant — Fibroblastoma, Giant Cell — Fibroblastomas, Giant Cell — Giant Cell Fibroblastomas — Giant Dermatofibrosarcoma Protuberans — Dermatofibrosarcoma Protuberan, Giant — Dermatofibrosarcoma Protuberans, Giant — Giant Dermatofibrosarcoma Protuberan — Protuberan, Giant Dermatofibrosarcoma — Protuberans, Giant Dermatofibrosarcoma — DFSP, Juvenile — DFSPs, Juvenile — Juvenile DFSP — Juvenile DFSPs — Familial Dermatofibrosarcoma Protuberans — Dermatofibrosarcoma Protuberans, Familial — Dermatofibrosarcoma Protuberan, Familial — Familial Dermatofibrosarcoma Protuberan — Protuberan, Familial Dermatofibrosarcoma — Protuberans, Familial Dermatofibrosarcoma — Dermatofibrosarcoma Protuberans, Giant Cell — Dermatofibrosarcoma Protuberans, Myxoid — Dermatofibrosarcoma Protuberan, Myxoid — Myxoid Dermatofibrosarcoma Protuberan — Myxoid Dermatofibrosarcoma Protuberans — Protuberan, Myxoid Dermatofibrosarcoma — Protuberans, Myxoid Dermatofibrosarcoma — DFSP, Myxoid — DFSPs, Myxoid — Myxoid DFSP — Myxoid DFSPs — Dermatofibrosarcoma Protuberans, Pigmented — Dermatofibrosarcoma Protuberan, Pigmented — Pigmented Dermatofibrosarcoma Protuberan — Pigmented Dermatofibrosarcoma Protuberans — Protuberan, Pigmented Dermatofibrosarcoma — Protuberans, Pigmented Dermatofibrosarcoma — Bednar's Tumor — Bednars Tumor — Tumor, Bednar's — DFSP, Pigmented — DFSPs, Pigmented — Pigmented DFSP — Pigmented DFSPs — Bednar Tumor — Tumor, Bednar