von Willebrand Diseases

von Willebrands sjukdomar

Engelsk definition

Group of hemorrhagic disorders in which the VON WILLEBRAND FACTOR is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion.

Svenska synonymer

Willebrands sjukdomar Vaskulär hemofili Vaskulär pseudohemofili Angiohemofili

Engelska synonymer

Hemophilia, Vascular Vascular Hemophilia Vascular Hemophilias Vascular Pseudohemophilia Pseudohemophilia, Vascular Pseudohemophilias, Vascular Vascular Pseudohemophilias Von Willebrand's Factor Deficiency Von Willebrand Disorder Disorder, Von Willebrand von Willebrand's Disease von Willebrand's Diseases Angiohemophilia Angiohemophilias von Willebrand Disease von Willebrand Disease, Recessive Form