En icke-inflammatorisk, fortskridande förträngning av de intrakraniella halsartärerna och bildande av nätliknande, kollaterala artärer ur Willis ring. Hjärnangiogram visar de rökpuffliknande bildningarna (moyamoya) vid hjärnbasen. Tillståndet kännetecknas av endotelhyperplasi och -fibros med förtjockning av artärväggarna. Sjukdomen drabbar främst barn, men kan även förekomma hos vuxna.
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.
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Progressive Intracranial Occlusive Arteropathy (Moyamoya) — Moyamoya Syndrome — Moya-Moya Disease — Disease, Moya-Moya — Moya Moya Disease — Cerebrovascular Moyamoya Disease — Moyamoya Disease, Primary — Disease, Primary Moyamoya — Moyamoya Diseases, Primary — Primary Moyamoya Disease — Primary Moyamoya Diseases — Moyamoya Disease, Classic — Classic Moyamoya Disease — Disease, Classic Moyamoya — Moyamoya Disease, Secondary — Secondary Moyamoya Disease