Mucinoses

Mucinoser

Svensk definition

Tillstånd som kännetecknas av ansamling av mucin (slem; mukopolysackarider) i hudvävnad. Fibroblasterna ansvarar för produktionen av sura mukopolysackarider (glykosaminoglykaner) i bindvävssystemets bassubstans. När fibroblasterna framställer onormalt stora mängder mukopolysackarider (hyaluronsyra, kondroitinsulfat eller heparin), så lagras dessa i höga halter i hudvävnaden.

Engelsk definition

Mucoid states characterized by the elevated deposition and accumulation of mucin (mucopolysaccharides) in dermal tissue. The fibroblasts are responsible for the production of acid mucopolysaccharides (GLYCOSAMINOGLYCANS) in the ground substance of the connective tissue system. When fibroblasts produce abnormally large quantities of mucopolysaccharides as hyaluronic acid, chondroitin sulfate, or heparin, they accumulate in large amounts in the dermis.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Mucinosis