Parkinson Disease, Postencephalitic

Parkinsons sjukdom, postencefalitisk

Svensk definition

Parkinsons sjukdom som följd av hjärninflammation, historiskt sett som följd av encephalitis lethargica (von Economos encefalit). Tidig ålder vid debut, snabbt fortskridande av symtom med efterföljande stabilisering och förekomst av olika neurologiska rubbningar (t ex sociopatiskt beteende, tickrubbnngar, muskelkramp, okulogyrisk kris, hyperfagi och bisarra rörelser skiljer tillståndet från primär Parkinsons sjukdom. Patologiska kännetecken inkluderar förlust av neuroner och glios i mitthjärna, subtalamus och hypotalamus.

Engelsk definition

Parkinsonism following encephalitis, historically seen as a sequella of encephalitis lethargica (Von Economo Encephalitis). The early age of onset, the rapid progression of symptoms followed by stabilization, and the presence of a variety of other neurological disorders (e.g., sociopathic behavior; TICS; MUSCLE SPASMS; oculogyric crises; hyperphagia; and bizarre movements) distinguish this condition from primary PARKINSON DISEASE. Pathologic features include neuronal loss and gliosis concentrated in the MESENCEPHALON; SUBTHALAMUS; and HYPOTHALAMUS. (From Adams et al., Principles of Neurology, 6th ed, p754)

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Parkinson Disease, Post-Encephalitic Parkinson Disease, Post Encephalitic Parkinsonian Syndrome, Postencephalitis Postencephalitis Parkinsonian Syndrome von Economo Encephalitis Type Parkinsonism Post-Encephalitic Parkinson Disease Post Encephalitic Parkinson Disease Postencephalitic Economo-Type Parkinsonism Economo-Type Parkinsonism, Postencephalitic Parkinsonism, Postencephalitic Economo-Type Postencephalitic Economo Type Parkinsonism Postencephalitic Parkinson Disease Postencephalitic Parkinsonism Encephalitis Lethargica Type Parkinsonism Parkinsonism, Postencephalitic Parkinsonism, Viral Meningoencephalitic Meningoencephalitic Parkinsonism, Viral Viral Meningoencephalitic Parkinsonism Parkinsonisms, Viral Meningoencephalitic