Engelsk definition
Abnormal thoracoabdominal VISCERA arrangement (visceral heterotaxy) or malformation that involves additional CONGENITAL HEART DEFECTS (e.g., heart isomerism; DEXTROCARDIA) and/or abnormal SPLEEN (e.g., asplenia and polysplenia). Irregularities with the central nervous system, the skeleton and urinary tract are often associated with the syndrome.
Svenska synonymer
Asplenia syndrom — Ivemarks syndrom — Vänster-isomerism — Höger-isomerism — Polysplenisyndrom — Situs ambiguus
Engelska synonymer
Heterotaxy Syndromes — Syndrome, Heterotaxy — Syndromes, Heterotaxy — Left Atrial Isomerism — Atrial Isomerism, Left — Atrial Isomerisms, Left — Isomerism, Left Atrial — Isomerisms, Left Atrial — Left Atrial Isomerisms — Right Atrial Isomerism — Atrial Isomerism, Right — Atrial Isomerisms, Right — Isomerism, Right Atrial — Isomerisms, Right Atrial — Right Atrial Isomerisms — Visceral Heterotaxy — Heterotaxies, Visceral — Heterotaxy, Visceral — Visceral Heterotaxies — Situs Ambiguus — Ambiguus, Situs — Situs Ambiguus Viscerum — Ambiguus Viscerum, Situs — Ambiguus Viscerums, Situs — Situs Ambiguus Viscerums — Viscerum, Situs Ambiguus — Viscerums, Situs Ambiguus — Asplenia Syndrome — Asplenia Syndromes — Syndrome, Asplenia — Syndromes, Asplenia — Asplenia with Cardiovascular Anomalies — Ivemark Syndrome — Syndrome, Ivemark — Right Atrial Isomerism with Asplenia — Situs Ambiguus with Asplenia — Polysplenia Syndrome — Polysplenia Syndromes — Syndrome, Polysplenia — Syndromes, Polysplenia — Left Atrial Isomerism with Polysplenia — Situs Ambiguus with Polysplenia