Heterotaxy Syndrome

Heterotaxisyndrom

Engelsk definition

Abnormal thoracoabdominal VISCERA arrangement (visceral heterotaxy) or malformation that involves additional CONGENITAL HEART DEFECTS (e.g., heart isomerism; DEXTROCARDIA) and/or abnormal SPLEEN (e.g., asplenia and polysplenia). Irregularities with the central nervous system, the skeleton and urinary tract are often associated with the syndrome.

Svenska synonymer

Asplenia syndrom Ivemarks syndrom Vänster-isomerism Höger-isomerism Polysplenisyndrom Situs ambiguus

Engelska synonymer

Heterotaxy Syndromes Syndrome, Heterotaxy Syndromes, Heterotaxy Left Atrial Isomerism Atrial Isomerism, Left Atrial Isomerisms, Left Isomerism, Left Atrial Isomerisms, Left Atrial Left Atrial Isomerisms Right Atrial Isomerism Atrial Isomerism, Right Atrial Isomerisms, Right Isomerism, Right Atrial Isomerisms, Right Atrial Right Atrial Isomerisms Visceral Heterotaxy Heterotaxies, Visceral Heterotaxy, Visceral Visceral Heterotaxies Situs Ambiguus Ambiguus, Situs Situs Ambiguus Viscerum Ambiguus Viscerum, Situs Ambiguus Viscerums, Situs Situs Ambiguus Viscerums Viscerum, Situs Ambiguus Viscerums, Situs Ambiguus Asplenia Syndrome Asplenia Syndromes Syndrome, Asplenia Syndromes, Asplenia Asplenia with Cardiovascular Anomalies Ivemark Syndrome Syndrome, Ivemark Right Atrial Isomerism with Asplenia Situs Ambiguus with Asplenia Polysplenia Syndrome Polysplenia Syndromes Syndrome, Polysplenia Syndromes, Polysplenia Left Atrial Isomerism with Polysplenia Situs Ambiguus with Polysplenia