Hereditary Angioedema Type III

Hereditärt angioödem typ II

Engelsk definition

A form of hereditary angioedema that occurs in women and is precipitated or worsened by high ESTROGEN levels. It is associated with mutations in the gene for FACTOR XII that result in its increased activity.

Svenska synonymer

Ärftligt angioöedem typ III Östrogenrelaterad HAE Östrogensensitiv hereditär angioödem

Engelska synonymer

Estrogen-Related HAE Estrogen Related HAE Estrogen-Related HAEs HAE, Estrogen-Related HAEs, Estrogen-Related Hereditary Angioedema with Normal C1 Inhibitor Activity Angioedema, Hereditary, Type III HAE with Normal C1 Inhibitor Concentration and Function Angioneurotic Edema, Hereditary, with Normal C1 Inhibitor Concentration and Function Estrogen-Sensitive Hereditary Angioedema Angioedema, Estrogen-Sensitive Hereditary Angioedemas, Estrogen-Sensitive Hereditary Estrogen Sensitive Hereditary Angioedema Estrogen-Sensitive Hereditary Angioedemas Hereditary Angioedema, Estrogen-Sensitive Hereditary Angioedemas, Estrogen-Sensitive Estrogen-Sensitive HAE Estrogen Sensitive HAE Estrogen-Sensitive HAEs HAE, Estrogen-Sensitive HAEs, Estrogen-Sensitive