Svensk definition
Medfödd avsaknad av den normala klafföppningen till lungartären. Tillståndet kännetecknas av förstorat hjärta, minskad kärllförsörjning i lungorna och högersidig kammaratrofi.
Pulmonary Atresia
Lungatresi
Engelsk definition
A congenital heart defect characterized by the narrowing or complete absence of the opening between the RIGHT VENTRICLE and the PULMONARY ARTERY. Lacking a normal PULMONARY VALVE, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, CYANOSIS, right ventricle atrophy, and abnormal heart sounds (HEART MURMURS).
Svenska synonymer
Pulmonalatresi
Engelska synonymer
Atresia, Pulmonary — Pulmonary Valve Atresia — Atresias, Pulmonary — Atresias, Pulmonary Valve — Pulmonary Atresias — Pulmonary Valve Atresias — Atresia, Pulmonary Valve — Valve Atresia, Pulmonary — Valve Atresias, Pulmonary