Desmoid Tumors

Aggressiv fibromatos

Svensk definition

En barnvariant av desmoidtumörer i eller utanför buken, kännetecknad av fasta, subkutana noduler som växer snabbt var som helst i kroppen, men som inte bildar metastaser. Hos vuxna kallas tumörformen bukfibromatos.

Engelsk definition

Locally aggressive tumors that form in the connective tissues of body with no known potential for metastasis. However, they are characterized by an infiltrative growth pattern, allowing invasion into nearby tissues and organs, particularly evident in patients with FAMILIAL ADENOMATOUS POLYPOSIS.

Svenska synonymer

Desmoid

Engelska synonymer

Desmoid Tumor Tumor, Desmoid Tumors, Desmoid Deep Fibromatoses Deep Fibromatose Fibromatose, Deep Fibromatoses, Deep Deep Fibromatosis Fibromatosis, Deep Desmoid Fibromatosis Desmoid Fibromatoses Fibromatoses, Desmoid Fibromatosis, Desmoid Desmoid-type Fibromatosis Desmoid-type Fibromatoses Desmoid type Fibromatosis Fibromatoses, Desmoid-type Fibromatosis, Desmoid-type Fibromatosis, Aggressive Aggressive Fibromatoses Aggressive Fibromatosis Fibromatoses, Aggressive Musculoaponeurotic Fibromatosis Fibromatoses, Musculoaponeurotic Fibromatosis, Musculoaponeurotic Musculoaponeurotic Fibromatoses Extra Abdominal Desmoid Tumor