Kronisk, medfödd iktyos med autosomalt recessiv nedärvning. Nyfödda är oftast inneslutna i ett lamellärt membran som fjällar av inom några få veckor. Fjällningen är fullt utbredd, med gråbruna, fyrsidiga fjäll som sitter fast i mitten, men har fria kanter. I vissa fall kan fjällen vara så tjocka att de liknar hornplattor.
A chronic, congenital ichthyosis inherited as an autosomal recessive trait. Infants are usually born encased in a collodion membrane which sheds within a few weeks. Scaling is generalized and marked with grayish-brown quadrilateral scales, adherent at their centers and free at the edges. In some cases, scales are so thick that they resemble armored plate.
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Erythroderma Ichthyosiforme, Nonbullous — Erythroderma Ichthyosiformes, Nonbullous — Ichthyosiforme, Nonbullous Erythroderma — Ichthyosiformes, Nonbullous Erythroderma — Nonbullous Erythroderma Ichthyosiforme — Nonbullous Erythroderma Ichthyosiformes — Congenital Nonbullous Ichthyosiform Erythroderma — Nonbullous Congenital Ichthyosiform Erythroderma — Ichthyosiform Erythroderma, Nonbullous Congenital — Nonbullous Congenital Lamellar Ichthyosis — Congenital Ichthyosiform Erythroderma, Nonbullous — Lamellar Ichthyosis — Ichthyoses, Lamellar — Ichthyose, Lamellar — Lamellar Ichthyose — Lamellar Ichthyoses — Harlequin Fetus — Fetus, Harlequin — Harlequin Ichthyosis — Harlequin Ichthyoses — Ichthyoses, Harlequin — Ichthyosis, Harlequin — Harlequin Baby Syndrome — Baby Syndrome, Harlequin — Baby Syndromes, Harlequin — Harlequin Baby Syndromes — Syndrome, Harlequin Baby — Syndromes, Harlequin Baby — Ichthyosis Congenita I — Ichthyosis, Lamellar, 1 — Lamellar Ichthyosis, Type 1 — Ichthyosis Congenita II — Congenita II, Ichthyosis — Congenita IIs, Ichthyosis — Ichthyosis Congenita IIs — Collodion Fetus — Fetus, Collodion — Desquamation of Newborn — Newborn Desquamation — Newborn Desquamations — Collodion Baby Syndrome — Baby Syndrome, Collodion — Baby Syndromes, Collodion — Collodion Baby Syndromes — Syndrome, Collodion Baby — Syndromes, Collodion Baby — Ichthyosis Congenita — Lamellar Exfoliation of Newborn — Newborn Lamellar Exfoliation — Newborn Lamellar Exfoliations