Engelsk definition
Thrombocytopenia occurring in the absence of toxic exposure or a disease associated with decreased platelets. It is mediated by immune mechanisms, in most cases IMMUNOGLOBULIN G autoantibodies which attach to platelets and subsequently undergo destruction by macrophages. The disease is seen in acute (affecting children) and chronic (adult) forms.
Svenska synonymer
Idiopatisk trombocytopen purpura
Engelska synonymer
Autoimmune Thrombocytopenia — Autoimmune Thrombocytopenias — Thrombocytopenia, Autoimmune — Thrombocytopenias, Autoimmune — Immune Thrombocytopenic Purpura — Immune Thrombocytopenic Purpuras — Purpura, Immune Thrombocytopenic — Purpuras, Immune Thrombocytopenic — Thrombocytopenic Purpura, Immune — Thrombocytopenic Purpuras, Immune — Thrombocytopenic Purpura, Autoimmune — Immune Thrombocytopenia — Immune Thrombocytopenias — Thrombocytopenia, Immune — Thrombocytopenias, Immune — Werlhof Disease — Disease, Werlhof — Werlhof's Disease — Disease, Werlhof's — Werlhofs Disease — Autoimmune Thrombocytopenic Purpura — Autoimmune Thrombocytopenic Purpuras — Purpura, Autoimmune Thrombocytopenic — Purpuras, Autoimmune Thrombocytopenic — Idiopathic Thrombocytopenic Purpura — Idiopathic Thrombocytopenic Purpuras — Purpura, Idiopathic Thrombocytopenic — Purpuras, Idiopathic Thrombocytopenic — Thrombocytopenic Purpura, Idiopathic — Thrombocytopenic Purpuras, Idiopathic — Purpura, Thrombocytopenic, Autoimmune