Ebstein Anomaly

Ebsteins anomali

Svensk definition

Medfödd missbildning av trikuspidalklaffen, där septum- och bakflikarna är fästa vid högra kammarens vägg.

Engelsk definition

A congenital heart defect characterized by downward or apical displacement of the TRICUSPID VALVE, usually with the septal and posterior leaflets being attached to the wall of the RIGHT VENTRICLE. It is characterized by a huge RIGHT ATRIUM and a small and less effective right ventricle.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Anomaly, Ebstein Ebstein's Malformation Ebstein Malformation Ebsteins Malformation Malformation, Ebstein's Ebstein's Anomaly Anomaly, Ebstein's Ebsteins Anomaly Familial Ebstein's Anomaly Ebstein's Anomaly, Familial Familial Ebstein Anomaly Familial Ebsteins Anomaly