Cryptogenic Organizing Pneumonia

Kryptogen organiserad pneumoni

Svensk definition

Sjukdom som tidigare betraktades som en interstitiell lunginflammation. Etiologin är oklar, men tillståndet kan hänga samman med giftiga gaser, infektion eller bindvävssjukdom. Till de kliniska symtom en hör hosta, dyspné och influensasymtom, ofta med typisk interstitiell pneumoni. Obstruktiva symtom förekommer endast hos rökare. Termen "organiserande" hänför sig till kvarstående lunginflammation s om leder till att det bildas fibrös vävnad i alveolerna.

Engelsk definition

An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.

Svenska synonymer

BOOP Bronchiolitis obliterans organiserade pneumoni

Engelska synonymer

Cryptogenic Organizing Pneumonias Organizing Pneumonia, Cryptogenic Pneumonia, Cryptogenic Organizing Bronchiolitis Obliterans Organizing Pneumonia BOOP Bronchiolitis Obliterans Organizing Pneumonia Primary Organizing Pneumonia Organizing Pneumonia, Primary Organizing Pneumonias, Primary Pneumonia, Primary Organizing Primary Organizing Pneumonias