A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
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Idiopathic Pulmonary Fibroses — Pulmonary Fibroses, Idiopathic — Idiopathic Fibrosing Alveolitis, Chronic Form — Fibrosing Alveolitis, Cryptogenic — Fibrocystic Pulmonary Dysplasia — Dysplasia, Fibrocystic Pulmonary — Fibrocystic Pulmonary Dysplasias — Pulmonary Dysplasia, Fibrocystic — Cryptogenic Fibrosing Alveolitis — Cryptogenic Fibrosing Alveolitides — Fibrosing Alveolitides, Cryptogenic — Pulmonary Fibrosis, Idiopathic — Familial Idiopathic Pulmonary Fibrosis — Idiopathic Pulmonary Fibrosis, Familial — Usual Interstitial Pneumonia — Interstitial Pneumonia, Usual — Usual Interstitial Pneumonias — Interstitial Pneumonitis, Usual — Pneumonitides, Usual Interstitial — Pneumonitis, Usual Interstitial — Usual Interstitial Pneumonitides — Usual Interstitial Pneumonitis