Idiopathic Pulmonary Fibrosis

Idiopatisk lungfibros

Engelsk definition

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

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Engelska synonymer

Idiopathic Pulmonary Fibroses Pulmonary Fibroses, Idiopathic Idiopathic Fibrosing Alveolitis, Chronic Form Fibrosing Alveolitis, Cryptogenic Fibrocystic Pulmonary Dysplasia Dysplasia, Fibrocystic Pulmonary Fibrocystic Pulmonary Dysplasias Pulmonary Dysplasia, Fibrocystic Cryptogenic Fibrosing Alveolitis Cryptogenic Fibrosing Alveolitides Fibrosing Alveolitides, Cryptogenic Pulmonary Fibrosis, Idiopathic Familial Idiopathic Pulmonary Fibrosis Idiopathic Pulmonary Fibrosis, Familial Usual Interstitial Pneumonia Interstitial Pneumonia, Usual Usual Interstitial Pneumonias Interstitial Pneumonitis, Usual Pneumonitides, Usual Interstitial Pneumonitis, Usual Interstitial Usual Interstitial Pneumonitides Usual Interstitial Pneumonitis