En utvecklingsanomali som brukar ge sig till känna som tilltagande andningssvikt under nyföddhetsperioden. Missbildningen består av en fokal lungdysplasi kännetecknad av en cystisk massa av bronkioländstrukturer. Dysplasin är indelad i tre olika typer (I, II, III), beroende på cyststorlek. Syn. CCAM.
An abnormality in lung development that is characterized by a multicystic mass resulting from an adenomatous overgrowth of the terminal BRONCHIOLES with a consequent reduction of PULMONARY ALVEOLI. This anomaly is classified into three types by the cyst size.
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Congenital Cystic Adenomatoid Malformation — Congenital Cystic Adenomatoid Malformation of Lung — Cystic Adenomatoid Malformation of Lung — Lung Malformation, Congenital Cystic Adenomatoid — Lung Malformation, Cystic Adenomatoid, Congenital — Congenital Cystic Adenomatoid Malformation, Type I — Congenital Cystic Adenomatoid Malformation, Type 1 — Congenital Cystic Adenomatoid Malformation, Type II — Congenital Cystic Adenomatoid Malformation, Type 2 — Congenital Cystic Adenomatoid Malformation, Type III — Congenital Cystic Adenomatoid Malformation, Type 3