Osteolysis, Essential

Essentiell osteolys

Svensk definition

Syndrom med upplösning av benvävnad utan påtagliga orsaker så som neoplasmer, infektioner eller trauma. Benvävnadsdestruktionen följer olika mönster: massiva (Gorhams sjukdom), multicentriska (Hajdu-Cheneys syndrom) eller karpala/tarsala.

Engelsk definition

Syndromes of bone destruction where the cause is not obvious such as neoplasia, infection, or trauma. The destruction follows various patterns: massive (Gorham disease), multicentric (HAJDU-CHENEY SYNDROME), or carpal/tarsal.

Svenska synonymer

Massiv osteolys Gorhams sjukdom Gorham-Stouts sjukdom Idiopatisk multicentrisk osteolys

Engelska synonymer

Essential Osteolyses Essential Osteolysis Osteolyses, Essential Disappearing Bone Disease Osteolysis, Idiopathic Multicentric Idiopathic Multicentric Osteolyses Idiopathic Multicentric Osteolysis Multicentric Osteolyses, Idiopathic Multicentric Osteolysis, Idiopathic Osteolysis, Massive Massive Osteolyses Massive Osteolysis Gorham-Stout Disease Gorham Stout Disease Cystic Angiomatosis Of Bone, Diffuse Gorham's Disease Gorhams Disease Gorham Disease