Castleman Disease

Castlemans sjukdom

Svensk definition

Stora, godartade, hyperplastiska lymfknutor. Den vanligare, hyalina kärlrika typen kännetecknas av små, hyalina kärlfolliklar och interfollikulär kapillärtillväxt. Plasmaceller är ofta närvarande och representerar en annan subtyp med IgM och IgA i plasmacellerna.

Engelsk definition

Large benign, hyperplastic lymph nodes. The more common hyaline vascular subtype is characterized by small hyaline vascular follicles and interfollicular capillary proliferations. Plasma cells are often present and represent another subtype with the plasma cells containing IgM and IMMUNOGLOBULIN A.

Svenska synonymer

Angiofollikulär lymfoid hyperplasi Castlemans tumör

Engelska synonymer

Giant Lymph Node Hyperplasia Angiofollicular Lymphoid Hyperplasia Angiofollicular Lymphoid Hyperplasias Hyperplasia, Angiofollicular Lymphoid Lymphoid Hyperplasia, Angiofollicular Castleman's Disease Castleman's Tumor Castlemans Tumor Castleman Tumor Tumor, Castleman's Hyperplasia, Giant Lymph Node Lymph Node Hyperplasia, Giant Angiofollicular Lymph Hyperplasia Angiofollicular Lymph Hyperplasias Hyperplasia, Angiofollicular Lymph Lymph Hyperplasia, Angiofollicular Castlemans Disease Disease, Castlemans Angiofollicular Lymph Node Hyperplasia