Cor Triatriatum

Cor triatriatum

Svensk definition

Medfödd missbildning i form av ett perforerat muskulärt membran i (vänstra) förmaket, som delar förmaket i en övre och en nedre kammare, så att hjärtat synes ha tre förmak.

Engelsk definition

A malformation of the heart in which the embryonic common PULMONARY VEIN was not incorporated into the LEFT ATRIUM leaving behind a perforated fibromuscular membrane bisecting the left atrium, a three-atrium heart. The opening between the two left atrium sections determines the degree of obstruction to pulmonary venous return, pulmonary venous and pulmonary arterial hypertension.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Cor Triatriatum Sinistrum Subdivided Left Atrium Atriums, Subdivided Left Atrium, Subdivided Left Left Atriums, Subdivided Left Atrium, Subdivided Subdivided Left Atriums Triatrial Heart Hearts, Triatrial Heart, Triatrial Triatrial Hearts