Porokeratosis

Porokeratos

Engelsk definition

A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Porokeratosis, Mibelli Mibelli Porokeratosis Porokeratosis of Mibelli Porokeratosis, Palmoplantar Palmoplantar Porokeratosis Keratoderma Palmoplantar, Punctate Type 2 Porokeratosis Palmaris et Plantaris Disseminata Porokeratosis Plantaris Palmaris et Disseminata Porokeratosis, Palmar, Plantar, And Disseminated 1 Porokeratosis Plantaris, Palmaris, Et Disseminata Type 2 Punctate PPK Porokeratosis, Linear Linear Porokeratosis Porokeratosis, Punctate Punctate Porokeratosis Porokeratosis, Disseminated Superficial Actinic 2 Porokeratosis, Disseminated Superficial Actinic, 2 Porokeratosis, Disseminated Superficial Actinic Disseminated Superficial Actinic Porokeratosis