Svensk definition
Ett epilepsisyndrom kännetecknat av triaden spädbarnskramp, hypsarytmi och avstannad psykomotorisk utveckling vid anfallsdebuten. De flesta fall visar sig vid åldern 3-12 månader, med krampyttringar som kortvariga flexor- och extensorrörelser i huvud, bål och extremiteter i kombination. Tillståndet har två former: en kryptogen (idiopatisk) och en symtomatisk (till följd av annan känd sjukdom, såsom livmoderinfektioner, nervsystemdefekter, ärftliga, metabola hjärnsjukdomar, för tidig födsel, perinatal asfyxi, tuberös skleros osv).
Engelsk definition
An epileptic syndrome characterized by the triad of infantile spasms, hypsarrhythmia, and arrest of psychomotor development at seizure onset. The majority present between 3-12 months of age, with spasms consisting of combinations of brief flexor or extensor movements of the head, trunk, and limbs. The condition is divided into two forms: cryptogenic (idiopathic) and symptomatic (secondary to a known disease process such as intrauterine infections; nervous system abnormalities; BRAIN DISEASES, METABOLIC, INBORN; prematurity; perinatal asphyxia; TUBEROUS SCLEROSIS; etc.). (From Menkes, Textbook of Child Neurology, 5th ed, pp744-8)
Svenska synonymer
Wests syndrom — Hypsarytmi — BNS-kramper — Salaam-anfall
Engelska synonymer
Infantile Spasm — Infantile Spasms — Lightning Attacks — Attack, Lightning — Attacks, Lightning — Lightning Attack — West Syndrome — Syndrome, West — Hypsarrhythmia — Hypsarrhythmias — Jackknife Seizures — Jackknife Seizure — Seizure, Jackknife — Seizures, Jackknife — Symptomatic Infantile Spasms — Infantile Spasm, Symptomatic — Infantile Spasms, Symptomatic — Spasm, Symptomatic Infantile — Spasms, Symptomatic Infantile — Symptomatic Infantile Spasm — Symptomatic West Syndrome — Syndrome, Symptomatic West — West Syndrome, Symptomatic — Salaam Attacks — Attacks, Salaam — Salaam Seizures — Seizures, Salaam — Spasmus Nutans — Cryptogenic Infantile Spasms — Cryptogenic Infantile Spasm — Infantile Spasm, Cryptogenic — Infantile Spasms, Cryptogenic — Spasm, Cryptogenic Infantile — Spasms, Cryptogenic Infantile — Cryptogenic West Syndrome — Syndrome, Cryptogenic West — West Syndrome, Cryptogenic — Nodding Spasm — Nodding Spasms — Spasm, Nodding — Spasms, Nodding