Svensk definition
En sällsynt hudtumör som förekommer hos äldre, oftare hos kvinnor.
Involverar huvudsakligen områden med apokrina körtlar som vulva,
skrotum och perianala områden. Differentialdiagnoser inkluderar skivepitelkarcinom och superficiella svampinfektioner.
Engelsk definition
A rare cutaneous neoplasm that occurs in the elderly. It develops more frequently in women and predominantly involves apocrine gland-bearing areas, especially the vulva, scrotum, and perianal areas. The lesions develop as erythematous scaly patches that progress to crusted, pruritic, erythematous plaques. The clinical differential diagnosis includes squamous cell carcinoma in situ and superficial fungal infection. It is generally thought to be an adenocarcinoma of the epidermis, from which it extends into the contiguous epithelium of hair follicles and eccrine sweat ducts. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1478)
Svenska synonymer
Inga svenska synonymer finns.
Engelska synonymer
Extra-Mammary Paget Disease — Extra Mammary Paget Disease — Extra-Mammary Paget's Disease — Extra Mammary Paget's Disease — Extra-Mammary Pagets Disease — Paget's Disease, Extramammary — Pagets Disease, Extramammary — Extramammary Paget's Disease — Extramammary Pagets Disease — Paget Disease, Extra-Mammary — Paget Disease, Extra Mammary — Paget's Disease, Extra-Mammary — Paget's Disease, Extra Mammary — Pagets Disease, Extra-Mammary — Paget Disease Extramammary — Extramammary, Paget Disease — Extramammary Paget Disease