Iduronidase

Iduronidas

Svensk definition

Ett enzym som hydrolyserar iduronosidbindningar i avsulfaterat dermatan. Brist på enzymet leder till Hurlers syndrom. EC 3.2.1.76.

Engelsk definition

An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

alpha-L-Idosiduronase alpha L Idosiduronase alpha-L-Iduronidase alpha L Iduronidase