Iduronate Sulfatase

Iduronatsulfatas

Svensk definition

Ett enzym som specifikt spjälkar iduronsyrans estersulfat. Brist på enzymet har påvisats vid Hunters syndrom, som kännetecknas av överskott på dermatansulfat och heparansulfat. EC 3.1.6.13.

Engelsk definition

An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome, which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Sulfatase, Iduronate Iduronate Sulfate Sulfatase Sulfatase, Iduronate Sulfate Sulfate Sulfatase, Iduronate Sulfoiduronate Sulfatase Sulfatase, Sulfoiduronate Hunter Corrective Factor Corrective Factor, Hunter Factor, Hunter Corrective Iduronatesulfate Sulfohydrolase Sulfohydrolase, Iduronatesulfate