Svensk definition
Ett enzym som specifikt spjälkar iduronsyrans estersulfat. Brist på enzymet har påvisats vid Hunters syndrom, som kännetecknas av överskott på dermatansulfat och heparansulfat. EC 3.1.6.13.
Iduronate Sulfatase
Iduronatsulfatas
Engelsk definition
An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome, which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13.
Svenska synonymer
Inga svenska synonymer finns.
Engelska synonymer
Sulfatase, Iduronate — Hunter Corrective Factor — Corrective Factor, Hunter — Factor, Hunter Corrective — Iduronate Sulfate Sulfatase — Sulfatase, Iduronate Sulfate — Sulfate Sulfatase, Iduronate — Iduronatesulfate Sulfohydrolase — Sulfohydrolase, Iduronatesulfate — Sulfoiduronate Sulfatase — Sulfatase, Sulfoiduronate