Ett pyridoxalfosfatenzym med flera funktioner. I det andra steget i cysteinbiosyntesen katalyserar det reaktionen mellan homocystein och serin, vilken ger cystationin och eliminering av vatten. Brist på detta enzym leder till hyperhomocysteinemi och homocystinuri. EC 4.2.1.22.
A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyzes the reaction of homocysteine with serine to form cystathionine with the elimination of water. Deficiency of this enzyme leads to HYPERHOMOCYSTEINEMIA and HOMOCYSTINURIA. EC 4.2.1.22.
Inga svenska synonymer finns.
Cystathionine beta Synthase — beta-Synthase, Cystathionine — Serine Sulfhydrase — Sulfhydrase, Serine — Cystathionine Synthetase — Synthetase, Cystathionine — beta-Thionase — beta Thionase