Ett enzym som katalyserar bildandet av karbamoylfosfat från ATP, koldioxid och ammoniak. Enzymet är specifikt för argininbiosyntesen eller ureacykeln. Frånvaro av enzymet kan ge upphov till karbamoylf osfatsyntas I-brist. EC 6.3.4.16.
An enzyme that catalyzes the formation of carbamoyl phosphate from ATP, carbon dioxide, and ammonia. This enzyme is specific for arginine biosynthesis or the urea cycle. Absence or lack of this enzyme may cause CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE. EC 6.3.4.16.
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Carbamyl Phosphate Synthase (Ammonia) — Carbamyl-Phosphate Synthase (Ammonia) — Carbamoyl-Phosphate Synthetase I — Synthetase I, Carbamoyl-Phosphate — Carbamoyl-Phosphate Synthetase (Ammonia) — Carbamoyl Phosphate Synthetase I — Carbamoylphosphate Synthetase I — Synthetase I, Carbamoylphosphate — CP Synthase I — Synthase I, CP