Immunoglobulin G4-Related Disease

Immunoglobulin G4-relaterad sjukdom

Engelsk definition

A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic role. It can affect multiple organs in highly variable presentations, characterized by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS and eventual organ damage.

Svenska synonymer

IgG4-associerad sjukdom IgG4-relaterad sjukdom

Engelska synonymer

Immunoglobulin G4 Related Disease Immunoglobulin G4-Related Diseases IgG4 Related Systemic Disease IgG4-RD IgG4-Associated Autoimmune Disease Autoimmune Disease, IgG4-Associated IgG4 Associated Autoimmune Disease IgG4-Associated Autoimmune Diseases IgG4-Related Disease IgG4 Related Disease IgG4-Related Diseases IgG4-Related Sclerosing Disease IgG4 Related Sclerosing Disease IgG4-Related Sclerosing Diseases Sclerosing Disease, IgG4-Related Immunoglobulin G4-Related Sclerosing Disease Immunoglobulin G4 Related Sclerosing Disease IgG4-Related Kidney Disease IgG4 Related Kidney Disease IgG4-Related Kidney Diseases Kidney Disease, IgG4-Related Immunoglobulin G4-Related Kidney Disease Immunoglobulin G4 Related Kidney Disease