A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic role. It can affect multiple organs in highly variable presentations, characterized by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS and eventual organ damage.
IgG4-associerad sjukdom — IgG4-relaterad sjukdom
Immunoglobulin G4 Related Disease — Immunoglobulin G4-Related Diseases — IgG4 Related Systemic Disease — IgG4-RD — IgG4-Associated Autoimmune Disease — Autoimmune Disease, IgG4-Associated — IgG4 Associated Autoimmune Disease — IgG4-Associated Autoimmune Diseases — IgG4-Related Disease — IgG4 Related Disease — IgG4-Related Diseases — IgG4-Related Sclerosing Disease — IgG4 Related Sclerosing Disease — IgG4-Related Sclerosing Diseases — Sclerosing Disease, IgG4-Related — Immunoglobulin G4-Related Sclerosing Disease — Immunoglobulin G4 Related Sclerosing Disease — IgG4-Related Kidney Disease — IgG4 Related Kidney Disease — IgG4-Related Kidney Diseases — Kidney Disease, IgG4-Related — Immunoglobulin G4-Related Kidney Disease — Immunoglobulin G4 Related Kidney Disease