An autosomal dominant skin disease characterized by transient and variable noninflammatory ERYTHEMA and hyperkeratosis. It has been associated with mutations in the genes that code for CONNEXINS. Erythrokeratodermia variabilis inherited in an autosomal recessive fashion has also been reported. Affected individuals often develop PALMOPLANTAR KERATODERMA.
Variabel erytrokeratodermi — Greithers sjukdom — Mendes da Costas syndrom
Mendes De Costa Syndrome — Erythrokeratodermia Figurata, Congenital Familial, in Plaques — Erythro et Keratodermia Variabilis — Erythrokeratodermia, Progressive Symmetric — Progressive Symmetric Erythrokeratodermia — Erythrokeratodermia Variabilis with Erythema Gyratum Repens — Erythrokeratodermia Figurata Variabilis — Greither Disease — Transgrediens et Progrediens Palmoplantar Keratoderma