Primary Myelofibrosis

Primär myelofibros

Engelsk definition

A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.

Svenska synonymer

Myelofibros Myeloid metaplasi

Engelska synonymer

Myelofibroses, Primary Myelofibrosis, Primary Primary Myelofibroses Bone Marrow Fibrosis Bone Marrow Fibroses Fibroses, Bone Marrow Fibrosis, Bone Marrow Myelofibrosis Myelofibroses Idiopathic Myelofibrosis Myeloid Metaplasia Metaplasia, Myeloid Metaplasias, Myeloid Myeloid Metaplasias Myelosclerosis Myeloscleroses Myelosis, Nonleukemic Myeloses, Nonleukemic Nonleukemic Myeloses Nonleukemic Myelosis Chronic Idiopathic Myelofibrosis Agnogenic Myeloid Metaplasia Agnogenic Myeloid Metaplasias Metaplasia, Agnogenic Myeloid Metaplasias, Agnogenic Myeloid Myeloid Metaplasia, Agnogenic Myeloid Metaplasias, Agnogenic Myelofibrosis With Myeloid Metaplasia