Nephrogenic Fibrosing Dermopathy

Nefrogen fibroserande dermopati

Svensk definition

Ett kroniskt, förvärvat, idiopatiskt och fortskridande hudutslag som har samband med njursvikt. Det åtföljs ibland av systemisk fibros. Patogenesen tycks ha flera orsaker, med inblandning av cirkulerande fibrocyter som förutsättning. Det finns ett starkt samband mellan åkomman och användning av gadoliniumhaltiga kontrastmedel.

Engelsk definition

A chronic, acquired, idiopathic, progressive eruption of the skin that occurs in the context of RENAL FAILURE. It is sometimes accompanied by systemic fibrosis. The pathogenesis seems to be multifactorial, with postulated involvement of circulating fibrocytes. There is a strong association between this disorder and the use of gadolinium-based contrast agents.

Svenska synonymer

Nefrogen systemisk fibros

Engelska synonymer

Dermopathies, Nephrogenic Fibrosing Dermopathy, Nephrogenic Fibrosing Fibrosing Dermopathies, Nephrogenic Fibrosing Dermopathy, Nephrogenic Nephrogenic Fibrosing Dermopathies Nephrogenic Systemic Fibrosis Fibroses, Nephrogenic Systemic Fibrosis, Nephrogenic Systemic Nephrogenic Systemic Fibroses Systemic Fibroses, Nephrogenic Systemic Fibrosis, Nephrogenic