Glutaryl-CoA Dehydrogenase

Glutaryl-CoA-dehydrogenas

Engelsk definition

A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Dehydrogenase, Glutaryl-CoA Glutaryl-Coenzyme A Dehydrogenase Dehydrogenase, Glutaryl-Coenzyme A Glutaryl Coenzyme A Dehydrogenase Glutaryl CoA Dehydrogenase CoA Dehydrogenase, Glutaryl Dehydrogenase, Glutaryl CoA