Svensk definition
Ett enzym av mitokondrieflavoprotein som katalyserar oxidationen av 3-metylbutanoyl-CoA till 3-metylbut-2-enoyl-CoA med hjälpav FAD som kofaktor. Defekter i detta enzym är förenade med isovalerisk acidemi (IVA). EC 1.3.99.10.
Isovaleryl-CoA Dehydrogenase
Isovaleryl-CoA-dehydrogenas
Engelsk definition
A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
Svenska synonymer
Inga svenska synonymer finns.
Engelska synonymer
Dehydrogenase, Isovaleryl-CoA — Isovaleryl CoA Dehydrogenase — CoA Dehydrogenase, Isovaleryl — Dehydrogenase, Isovaleryl CoA — Isovaleryl-Coenzyme A Dehydrogenase — Dehydrogenase, Isovaleryl-Coenzyme A — Isovaleryl Coenzyme A Dehydrogenase