Succinate-Semialdehyde Dehydrogenase

Succinat-semialdehyddehydrogenas

Engelsk definition

An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA).

Svenska synonymer

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Engelska synonymer

Dehydrogenase, Succinate-Semialdehyde Succinate Semialdehyde Dehydrogenase Dehydrogenase, Succinate Semialdehyde Semialdehyde Dehydrogenase, Succinate Succinic Semialdehyde Dehydrogenase Dehydrogenase, Succinic Semialdehyde Semialdehyde Dehydrogenase, Succinic NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase