beta-Mannosidase

Betamannosidas

Engelsk definition

An enzyme that catalyzes the hydrolysis of terminal, non-reducing beta-D-mannose residues in beta-D-mannosides. The enzyme plays a role in the lysosomal degradation of the N-glycosylprotein glycans. Defects in the lysosomal form of the enzyme in humans result in a buildup of mannoside intermediate metabolites and the disease BETA-MANNOSIDOSIS.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

beta Mannosidase beta-Mannanase beta Mannanase manA protein (beta-Mannosidase) beta-D-Mannosidase beta D Mannosidase