N-Acetylgalactosamine-4-Sulfatase

N-acetylgalaktosamin-4-sulfatas

Engelsk definition

An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

N-Acetylgalactosamine 4-Sulfatase 4-Sulfatase, N-Acetylgalactosamine N Acetylgalactosamine 4 Sulfatase N-Acetylgalactosamine-4-sulphate Sulphatase N Acetylgalactosamine 4 sulphate Sulphatase Sulphatase, N-Acetylgalactosamine-4-sulphate N-Acetylgalactosamine-4-sulfate Sulfatase N Acetylgalactosamine 4 sulfate Sulfatase Sulfatase, N-Acetylgalactosamine-4-sulfate Arylsulfatase B Arylsulfatase B2 B2, Arylsulfatase Arylsulfatase B1 B1, Arylsulfatase