Hernias, Diaphragmatic, Congenital

Medfött diafragmabråck

Engelsk definition

Protrusion of abdominal structures into the THORAX as a result of embryologic defects in the DIAPHRAGM often present in the neonatal period. It can be isolated, syndromic, non-syndromic or be a part of chromosome abnormality. Associated pulmonary hypoplasia and PULMONARY HYPERTENSION can further complicate stabilization and surgical intervention.

Svenska synonymer

Kongenitalt diafragmabråck Bochdalek bråck Morgagnis bråck

Engelska synonymer

Agenesis of Hemidiaphragm Hemidiaphragm Ageneses Hemidiaphragm Agenesis Unilateral Agenesis of Diaphragm Diaphragm Unilateral Ageneses Diaphragm Unilateral Agenesis Congenital Diaphragmatic Defect Congenital Diaphragmatic Defects Defect, Congenital Diaphragmatic Defects, Congenital Diaphragmatic Diaphragmatic Defect, Congenital Diaphragmatic Defects, Congenital Congenital Diaphragmatic Hernia Diaphragmatic Hernia, Congenital Diaphragmatic Hernias, Congenital Hernia, Congenital Diaphragmatic Hernias, Congenital Diaphragmatic Congenital Diaphragmatic Hernias Morgagni Hernias Hernias, Morgagni Morgagni's Hernias Morgagnis Hernias Morgagni Hernia Hernia, Morgagni Morgagni's Hernia Hernia, Morgagni's Hernias, Morgagni's Morgagnis Hernia Bochdalek Hernias Bochdalek Hernia Hernia, Bochdalek Hernias, Bochdalek