Svensk definition
Familjärt eller idiopatiskt högt blodtryck i lungcirkulationen som inte är orsakat av någon annan sjukdom.
Familial Primary Pulmonary Hypertension
Familjär primär pulmonell hypertension
Engelsk definition
Familial or idiopathic hypertension in the PULMONARY CIRCULATION which is not secondary to other disease.
Svenska synonymer
Idiopatisk pulmonell hypertension — Idiopatisk pulmonell arteriell hypertension — Familjär pulmonell arteriell hypertension — Primär pulmonell hypertension 1
Engelska synonymer
Heritable Pulmonary Arterial Hypertension — Idiopathic Pulmonary Arterial Hypertension — Idiopathic Pulmonary Hypertension — Hypertension, Idiopathic Pulmonary — Pulmonary Hypertension, Idiopathic — Primary Pulmonary Hypertension — Hypertension, Primary Pulmonary — Pulmonary Hypertension, Primary — Pulmonary Hypertension, Primary, Dexfenfluramine-Associated — Pulmonary Hypertension, Primary, Fenfluramine-Associated — Pulmonary Hypertension, Primary, 1, With Hereditary Hemorrhagic Telangiectasia — Pph1 With Hht — Pulmonary Hypertension, Primary, 1