Cardiomyopathy, Restrictive

Kardiomyopati, restriktiv

Svensk definition

Hjärtmuskelsjukdom med stela kammarväggar, vilket begränsar kamrarnas förmåga att fyllas. Tillståndet ger onormal diastolisk funktion, men normal eller nästan normal systolisk funktion.

Engelsk definition

A form of CARDIAC MUSCLE disease in which the ventricular walls are excessively rigid, impeding ventricular filling. It is marked by reduced diastolic volume of either or both ventricles but normal or nearly normal systolic function. It may be idiopathic or associated with other diseases (ENDOMYOCARDIAL FIBROSIS or AMYLOIDOSIS) causing interstitial fibrosis.

Svenska synonymer

Restriktiv kardiomyopati

Engelska synonymer

Cardiomyopathies, Restrictive Restrictive Cardiomyopathies Restrictive Cardiomyopathy Familial Restrictive Cardiomyopathy