Factor XI Deficiency

Faktor XI-brist

Svensk definition

Brist på blodkoagulationsfaktor XI (även kallad plasmatromboplastinförstadium eller PTA eller antihemofilifaktor C) som leder till en systemisk blodlevringsdefekt, benämnd hemofili C eller Rosenthals syndrom, vilken kan påminna om klassisk hemofili.

Engelsk definition

A hereditary deficiency of blood coagulation factor XI (also known as plasma thromboplastin antecedent or PTA or antihemophilic factor C) resulting in a systemic blood-clotting defect called hemophilia C or Rosenthal's syndrome, that may resemble classical hemophilia.

Svenska synonymer

Inga svenska synonymer finns.

Engelska synonymer

Deficiency, Factor Eleven Deficiencies, Factor Eleven Factor Eleven Deficiencies Factor 11 Deficiency Factor Eleven Deficiency Plasma Thromboplastin Antecedent Deficiency Hemophilia C Rosenthal's Syndrome Rosenthal's Syndromes Rosenthals Syndrome Syndrome, Rosenthal's Rosenthal Syndrome Rosenthal Syndromes Syndrome, Rosenthal Deficiency, Factor 11 Deficiencies, Factor 11 Factor 11 Deficiencies Deficiency, Factor XI Deficiencies, Factor XI Factor XI Deficiencies